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KMID : 0213520170310030263
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Korean Journal of Ophthalmology
2017 Volume.31 No. 3 p.263 ~ p.267
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Ophthalmologic Features of Lennox-Gastaut Syndrome
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Kim Bo-Hee
Yu Young-Suk
Kim Seong-Joon
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Abstract
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Purpose: To describe the characteristics and frequency of ophthalmologic findings in patients with Lennox-Gastaut syndrome (LGS).
Methods: The medical records of patients diagnosed with LGS at Seoul National University Children's Hospital from January 2004 to August 2014 were retrospectively reviewed. The records of 34 patients (mean age ± standard deviation, 2.66 ± 3.51 years; male, 58.8%) were reviewed. The primary measure was the incidence of ophthalmologic manifestations.
Results: Of the 34 patients, 88.2% had at least one ocular abnormality. Refractive error (52.9%) was the most frequently observed ophthalmologic manifestation in patients with LGS, followed by strabismus (32.4%), cortical visual impairment (23.5%), and retinopathy of prematurity (8.8%). Among these cases, seven patients had exotropia and three had esotropia.
Conclusions: LGS is a childhood-onset epileptic encephalopathy with variable ophthalmologic manifestations, the most frequent being refractive errors. Patients with suspected LGS should be examined regularly because ophthalmological features can change during their disease course.
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KEYWORD
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Epilepsy, Eye manifestations, Lennox-Gastaut syndrome
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