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KMID : 0311119690100020162
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Yonsei Medical Journal
1969 Volume.10 No. 2 p.162 ~ p.169
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Cushing´s Syndrome in Infancy
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Kim, Pyung Kil
Chung, Ki Sup/Yun, Duk Jin
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Abstract
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Cushing´s syndrome is very rare in infancy, especially in Korea. We observed a case of Cushing´s syndrome in a one year and 2 month old female baby with the complaints of a 3 months history of obesty and hirsutism and 2 months history of polyphagia.
There were retarded bone age, hypertension, increased urinary excretion of 17-hydroxycorticosteroid and 17-ketosteroid and eosinopenia but no thymic shadow in the chest X-ray. There was no response to the dexamethasone test (2 mg divided in 4 doses orally for 2 days), which suggested an adrenal tumor. Intravenous pyelography showed that the left kidney was displaced downward as compared to the right kidney and there was a hen-egg sized radio-opaque shadow at the upper pole of the left kidney suggesting a left adrenal tumor.
The tumor, reported as a benign adenoma pathologically, was . removed successfully by anterior abdominal approach. Hypertension, eosinopenia and hypokalemia were raturned to normal from 3 days after surgery but 17-hydroxycorticosteroid and 17-ketosteroid were returned to normal from 2 weeks after surgery. We have presented this case and have reviewed the literature.
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KEYWORD
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