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KMID : 0311120010420010142
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Yonsei Medical Journal
2001 Volume.42 No. 1 p.142 ~ p.146
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Classical Malignant Rhabdoid Tumor of Central Nervous System in 9-year-old Korean
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Hee Kyung Chang
Jung H Kim
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Abstract
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A Malignant rhabdoid tumor (MRT) arising in the right temporoparietal lobe of a 9-year-old boy is described along with the results of an immunohistochemical study. The patient initially sought medical attention for a ptosis and right sided headache. The child underwent a subtotal resection of the tumor, followed by radiotherapy and systemic chemotherapy, but died three years after surgery. A MRT, a primary neoplasm of the central nervous system (CNS), is an entity of unknown histogenesis with a dismal prognosis, which only occurs in early childhood. Histologically similar tumors with more varied morphological features have been designated as an atypical teratoid/rhabdoid tumor. However, a classical MRT is extremely rare in the CNS and our case represents a classical CNS MRT.
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KEYWORD
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