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KMID : 0338420000150010085
The Korean Journal of Internal Medicine
2000 Volume.15 No. 1 p.85 ~ p.88
Dermatomyositis without elevation of creatine kinase presented as bronchiolitis obliterans organizing pneumonia
Young Ho Lee
Seong Jae Choi/Jong Dae Ji/Jae Jeong Shim/Kyung Ho Kang/Hyun Deuk Cho¢Ó/Han Kyeom Kim/Gwan Gyu Song
Abstract
A case of dermatomyositis presented as bronchiolitis obliterans organizing pneumonia has been rarely reported. We describe a 46-year-old female patient with dermatomyositis without elevation of creatine kinase presented as bronchiolitis obliterans organizing pneumonia. She was treated with prednisolone and azathioprine. Over a 2-year follow-up she has had no elevation of creatine kinase. The patient remains asymptomatic and has no medication for dermatomyositis and bronchiolitis obliterans organizing pneumonia two years after initial treatment. It has been suggested that the prognosis of dermatomyositis without creatine kinase elevation may be poor. Because the prognosis of bronchiolitis obliterans organizing pneumonia is generally believed to be good, we tentatively suggest that the normal value of creatine kinase in dermatomyositis does not always seem to herald a poor prognosis, an associated malignancy or severe interstitial lung disease.
KEYWORD
Dermatomyositis, Brochiolitis Obliterans Organizing Pneumonia,
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