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KMID : 0368120100400120684
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Korean Circulation Journal
2010 Volume.40 No. 12 p.684 ~ p.686
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A Case of a Pulmonary Arteriovenous Malformation With Ebstein’s Anomaly
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Park Kwon-Oh
Kim Chang-Hwan
Lim Dal-Soo
Ro Young-Moo
Park Jong-Won
Chun Seung-Yun
Lim Seung-Jin
Cho Hyun-Jung
Lee Sang-Ho
Kim Sung-Eun
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Abstract
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A pulmonary arteriovenous malformation (PAVM) is a rare pulmonary vascular anomaly presenting as dyspnea or recurrent epistaxis. Ebstein’s anomaly (EA), a congenital cardiac malformation, is also a rare condition. There have been no reports concerning the co-existence of PAVM with hereditary hemorrhagic telangiectasia (HHT) and EA. A 40-year-old woman was admitted with a 2-month history of increasing dyspnea and several years of recurrent epistaxis. On transthoracic echocardiography, she was diagnosed with EA and agreed to undergo surgical treatment. A chest CT angiography showed a 12-mm serpig-inous vascular structure suspicious for a PAVM and a liver CT suggested HTT. Although it is unclear whether or not a concur-rent PAVM and EA have an embryologic or genetic relationship, we report a case of a PAVM with EA. Further genetic and em-bryonic studies are needed to identify a possible relationship of the two medical conditions.
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KEYWORD
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Arteriovenous malformation ration, Lung, Telangiectasia, hereditary hemorrhagic, Ebstein anomaly
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