KMID : 0368120120420080571
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Korean Circulation Journal 2012 Volume.42 No. 8 p.571 ~ p.574
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Cardiac Sarcoidosis Presenting With Complete Atrioventricular Block and Sustained Monomorphic Ventricular Tachycardia
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Lee Joo-Myung
Oh Il-Young Choi Dong-Ju
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Abstract
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Sarcoidosis is a rare but potentially fatal multisystem granulomatous disease of unknown etiology. While a number of clinical manifestations may develop, cardiac involvement (prior to or coincident with sarcoidosis of other organs) is an important prognostic factor. Recently, we encountered a patient with cardiac sarcoidosis who presented with complete atrioventricular (AV) block and sustained ventricular tachycardia. An implantable cardioverter-defibrillator was inserted as a precautionary measure for ventricular tachycardia and symptomatic complete AV block. 18F-fluoro-2-deoxyglucose positron emission tomography confirmed a dramatic response to high-dose steroid at four weeks, as demonstrated by a marked decrease in cardiac sarcoid activity from baseline status.
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KEYWORD
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Sarcoidosis, Heart failure, Magentic resonance imaging, Tachycardia, ventricular
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