KMID : 0368120170470020282
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Korean Circulation Journal 2017 Volume.47 No. 2 p.282 ~ p.285
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Catheter Ablation of Ventricular Tachycardia/Fibrillation in a Patient with Right Ventricular Amyloidosis with Initial Manifestations Mimicking Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy
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Chung Fa Po
Lin Yenn Jiang Kuo Ling Chen Shih Ann
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Abstract
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Differentiating arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) from other cardiomyopathies is clinically important but challenging. Although the modified Task Force Criteria can facilitate diagnosis of ARVD/C according to clinical manifestations, histopathological examination plays a pivotal role in excluding other diseases that can mimic ARVD/C. Here, we report a patient with amyloidosis that initially presented similarly to ARVD/C. The diagnosis was confirmed by endomyocardial biopsy, and catheter ablation eliminated the ventricular tachyarrhythmias through an epicardial approach.
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KEYWORD
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Amyloidosis, Arrhythmogenic right ventricular cardiomyopathy-dysplasia, Catheter ablation, Biopsy, Ventricular tachycardia
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