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KMID : 0390220000110010109
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Journal of Clinical Otolaryngology, Head and Neck Surgery
2000 Volume.11 No. 1 p.109 ~ p.114
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A Case of Fibrous Dysplasia of the Temporal Bone
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채세용/Sayong Chae
노혜일/이종우/류재영/정은선/Heil Noh/Jong Woo Lee/Jae Joung Ryu/Eun Sun Jeong
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Abstract
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Fibrous dysplasia is a bone disorder of unknown etiology in which normal bone is replaced with fibrotic tissue
and disorganized immature bone trabecular. The disease has three variants ; monostotic, polyostotic, and
Albright's syndrome. Monostotic fibrous dysplasia espcially involving mainly squama in temporal bone is rare.
The clinical course of them is unpredictable. Monostotic form arises usually in childhood and often come to an
arrest at puberty. Polyostotic from without endocrine dyfunction tends to appear at a slightly earlier age than
the monostotic from and may progress into middle age. Mostly their involvement is unilateral. Monostotic form
involving temporal bone is associated with conductive hearing loss attributable to compression of the external
auditory canal. Potential problems include cholesteatoma, recurrence and malignant transfromation. We report
a case of monostotic fibrous dydplasia of temporal bone involving mainly squama, which is successfully treated
with canaloplasty and skin graft. We also observed the eletron microscopic findings.
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KEYWORD
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