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KMID : 1100320170340010137
Yeungnam University Journal of Medicine
2017 Volume.34 No. 1 p.137 ~ p.139
Dermatomyositis sine dermatitis, a rare phenotype of idiopathic inflammatory myopathy
Park Jin-Sung

Park Ji-Young
Abstract
Dermatomyositis (DM) is characterized by progressive proximal limb weakness and typical skin manifestations. The histological findings that show perifascicular atrophy and deposition of membrane attack complex are pathognomic features of DM. Dermatomyositis is categorized into classical DM and non-classical DM, which includes amyopathic DM and DM sine dermatitis. DM sine dermatitis is seldom described because of its rarity, making the diagnosis more challenging. We report a case of DM sine dermatitis, a rare phenotype of DM.
KEYWORD
Dermatomyositis, Sine dermatitis, Skin manifestation, Perifascicular atrophy, Diagnostic criteria
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