|
KMID : 1225120110030010036
|
|
Vascular Neurology
2011 Volume.3 No. 1 p.36 ~ p.39
|
|
|
Creutzfeldt-Jakob Disease Presenting with Isolated Visual Complaints: Heidenhain’s Variant
|
|
Yang Young-Soon
Joo Jae-Jeong
Lee Sun-Hwa
Hwang Jung-Yun
Ha Sang-Won
Han Jung-Ho
Cho Eun-Kyoung
Kim Doo-Eung
|
|
|
Abstract
|
|
|
|
Heidenhain variant of Creutzfeldt-Jakob disease (CJD) may include visual field defects, visual hallucinations, visual agnosia, cortical blindness, and abnormal color or visuospatial perception. We report a 47-year-old man presenting with visual symptoms, prosopagnosia, simultagnosia. Myoclonus was synchronous with generalized periodic epileptiform discharges on electroencephalography. Diffusion-weighted magnetic resonance brain images showed increased signal intensity in the bilateral caudate and putamen, both occipital cortices, and left frontal and temporal cortices. 14-3-3 protein was positive in the cerebrospinal fluid. The Heidenhain variant of CJD should be considered in patients with isolated visual complaints and either.
|
|
|
KEYWORD
|
|
|
Creutzfeldt-Jakob disease, Heidenhain’s variant
|
|
|
FullTexts / Linksout information
|
|
|
|
|
|
Listed journal information
|
|
|
|