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KMID : 0363220240620010042
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Korean Journal of Dermatology
2024 Volume.62 No. 1 p.42 ~ p.45
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Adult-Onset Still’s Disease with Atypical Persistent Rash and Histologic Findings of Neutrophilic Urticarial Dermatosis
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Park Yu-Jeong
Shim Hui-Young
Choi Woo-Kyoung
Sim Hyun-Bo
Hong Jong-Soo
Lee Ai-Young
Lee Seung-Ho
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Abstract
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Adult-onset Still’s disease (AOSD) is a rare systemic inflammatory disease characterized by spiking fever, arthralgia, skin rashes, and hyperferritinemia. The rash is usually salmon-colored, non-itchy, accompanied by fever, and disappears with an improvement of fever. However, in some cases, the rash persisted regardless of fever. Here, we present a case of AOSD with an atypical persistent rash that showed histological findings resembling those of neutrophilic urticarial dermatosis. The patient was a 60-year-old woman with high fever, arthralgia, and a persistent flagellated skin rash. Despite systemic steroid treatment, the patient developed a serious complication: macrophage activation syndrome. Since this case presented with an atypical persistent rash with histological resemblance to neutrophilic urticarial dermatosis, we report its contribution to the further study of AOSD.
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KEYWORD
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Adult-onset Still’s disease, Neutrophilic urticarial dermatosis
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