KMID : 0364020070400040297
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Korean Journal of Thoracic and Cardiovascular Surgery 2007 Volume.40 No. 4 p.297 ~ p.300
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Dysfunction of the Prosthetic Aortic Valve in Idiopathic Hypereosinophilic Syndrome -A case report-
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Park Chong-Bin
Yoo Dong-Gon Seong Kyu-Wan Jung Sang-Sig Kang Gil-Hyun Kim Chong-Wook
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Abstract
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Idiopathic hypereosinophilic syndrome is a rare systemic, leukoproliferative disorder characterized by eosinophil- mediated tissue injury causing multiple organ failure, including the heart. Cardiac involvement occurs in more than 75% of patients with hypereosinophilic syndrome. Cardiac manifestations include subendocardial fibrosis, thrombus leading to peripheral emboli, restrictive cardiomyopathy, and valvular dysfunction. It is more common in men than in women (9£º1), and trends to present between the ages of 20 and 50 years. Presentation in childhood is unusual. We report for the first time a case of a 58-year-old man with idiopathic hypereosinophilic syndrome manifested by prosthetic aortic valve dysfunction that was successfully treated by steroid and hydroxyurea therapy after surgical valvular replacement.
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KEYWORD
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Hypereosinophilic syndrome, idiopathic, Aortic valve, surgery
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