KMID : 0367419770180060054
|
|
Journal of Korean Pediatric Society 1977 Volume.18 No. 6 p.54 ~ p.58
|
|
Ivemark¢¥s Syndrome 4 Cases
|
|
À̼øÀÏ/Lee, Soon Il
ÀÌ¿ì±æ/°ºÎ°æ/À̼±Èñ/À̽±Ô/Áøµ¿½Ä/À±´öÁø/Liegh, Woo Gill/Kang, Bu Kyung/Lee, Sun Hee/Lee, Sung Kyu/Chin, Dong Shik/Yun, Duk Jin
|
|
Abstract
|
|
|
Ivemark¢¥s syndrome is rare disease and characterized by congenital absence of the spleen associated with characteristic group of anomalies of the cardiovascular and gastroenteric systems.
We had experienced 4 cases of Ivemark¢¥s yndrome: Case 1 had asplenia, situs inversus, dextrocardia, ASD, and pulmonary stenosis; Case 2 had asplenia, bilobulated liver, centraly located stomach but deviated to right side, single ventrilce, and transposition of the great vessels with pulmonary atresia; Case 3 had asplenia, bilobulated liver, rentraly located stcmach but deviated to left side, tricuspid atresia, high VSD, hypoplasia of right ventricle, and right sided aortic arch; Case 4 had asplenia, bilobulated liver, dextrocardia, single ventricle, and truncus arteriosus.
We had diagnosed these cases by EKG, chest -K-ray, cardiac catheterization with cardiac angiogram. and liver and spleen scanning.
|
|
KEYWORD
|
|
|
|
FullTexts / Linksout information
|
|
|
|
Listed journal information
|
|
|
|