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KMID : 0390620000080010087
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Journal of Cardiovascular Ultrasound
2000 Volume.8 No. 1 p.87 ~ p.92
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A Case of Systemic Amyloidosis
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Kim Kyoung-Hee
Yun Kyeong-Ho
Choi Chang-Soo
Song Woo-Kern
Oh Seok-Kyu
Jeong Jin-Won
Park Yang-Kyu
Park Ock-Kyu
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Abstract
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Systemic amyloidosis is an uncommon disease characterized by deposits of fibrillar aggregates of monoclonal immunoglobuloin light chains in vital organs. This amyloid deposit cause cardiac or renal dysfunction and ultimately, death. Cardiac amyloidosis may be asymptomatic or important causes of progressive heart failure and refractory arrhythmia. Cardiac involvement from AL amyloidosis is rapidly fatal. The amyloidoses are classified according to the biochemical nature of the fibril-forming protein. Cardiac amyloidosis is common in primary (AL) and heterofamilial amyloidosis and very rare in the secondary (AA) form. As we experienced a case of systemic amyloidosis affected heart, liver and kidney, which was confirmed by histology. We present a 57-year-old female case with literature review.
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KEYWORD
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Systemic amyloidosis
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